Management of bladder exstrophy in an adolescent girl: a case report
DOI:
https://doi.org/10.13181/mji.cr.215249Keywords:
adolescent, bicornuate uterine, bladder exstrophy, case managementAbstract
Bladder exstrophy (BE) is a very rare congenital abnormality, especially in girls. We reported a 17-year-old girl with protruded bladder and urinary incontinence. Her vaginal orifice appeared stenotic and shifted anteriorly. She had an incomplete labia minora, short perineum, and anterior displacement of the anus. The pelvic radiography showed a pubic diastasis with a manta ray sign, and the ultrasonography examination showed a bicornuate uterus. She had undergone a functional reconstruction surgery with cystectomy, ileal conduit, appendectomy, and vaginoplasty along with the advancement of abdominal flap reconstruction with multiple Z-plasty. Functionally, she was able to urinate through the ileal conduit comfortably, had a regular menstrual cycle with minimal pain, had a wider vaginal canal, and had a smooth blood flow. Aesthetically, she had a good lower abdomen appearance, remained dry, and had an odorless urine. In clinical practice, this rare case report can provide additional knowledge and management of the same cases with effective results.
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Fishel-Bartal M, Perlman S, Messing B, Bardin R, Kivilevitch Z, Achiron R, et al. Early diagnosis of bladder exstrophy: quantitative assessment of a low-inserted umbilical cord. J Ultrasound Med. 2017;36(9):1801-5. https://doi.org/10.1002/jum.14212
Borer JG, Diamond DA. Bladder extrophy handbook. Boston: Boston Children's Hospital's. 2015. p. 1-32.
Kulkarni B, Chaudhari N. Embryogenesis of bladder extrophy: a new hypothesis. J Indian Assoc Pediatr Surg. 2008;13(2):57-60. https://doi.org/10.4103/0971-9261.43017
Ebert AK, Reutter H, Ludwig M, Rösch WH. The exstrophy-epispadias complex. Orphanet J Rare Dis. 2009;4:23. https://doi.org/10.1186/1750-1172-4-23
Lal NR, Borpatragohain DJ, Bhuyan MH. Bladder exstrophy: a rare case report. IOSR J Dent Med Sci. 2018;17(7):01-3. https://doi.org/10.9790/0853-1707170103
Massanyi EZ, Gearhart JP, Kost-Byerly S. Perioperative management of classic bladder exstrophy. Res Rep Urol. 2013;5:67-75. https://doi.org/10.2147/RRU.S29087
Apte AV, Saran R. Bladder exstrophy. People's J Sci Res. 2009;2(2):35-9.
Baradaran N, Gearhart JP. Bladder exstrophy-epispadias-cloacal exstrophy complex: a contemporary overview. Neoreviews. 2010;11(12):e705-13. https://doi.org/10.1542/neo.11-12-e705
Smeulders N, Woodhouse CR. Neoplasia in adult exstrophy patients. BJU Int. 2001;87(7):623-8. https://doi.org/10.1046/j.1464-410x.2001.02136.x
Ko JS, Lue K, Friedlander D, Baumgartner T, Stuhldreher P, DiCarlo HN, et al. Cystectomy in the pediatric exstrophy population: indications and outcomes. Urology. 2018;116:168-71. https://doi.org/10.1016/j.urology.2017.09.009
Nerli RB, Kamat GV, Alur SS, Koura A, Prabha V, Amarkhed SS. Bladder exstrophy in adulthood. Indian J Urol. 2008;24(2):164-8. https://doi.org/10.4103/0970-1591.40609
Cervellione RM, Philips T, Baradaran N, Asanuma H, Mathews RI, Gearhart JP. Vaginoplasty in the female exstrophy population: outcomes and complications. J Pediatr Urol. 2010;6(6):595-9. https://doi.org/10.1016/j.jpurol.2010.01.011
Mansour AM, Sarhan OM, Helmy TE, Awad B, Dawaba MS, Ghali AM. Management of bladder exstrophy epispadias complex in adults: is abdominal closure possible without osteotomy? World J Urol. 2010;28(2):199-204. https://doi.org/10.1007/s00345-009-0436-7
Amin KV, Tiwari N, Goel A, Chauhan AR. Pregnancy in case of exstrophy of bladder. Int J Reprod Contracept Obstet Gynecolo. 2017;6(4):1676-8. https://doi.org/10.18203/2320-1770.ijrcog20171453
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