Atypical orbital primary optic nerve sheath meningioma with severe disfiguring proptosis: an alternative surgical approach

Authors

  • Sylves Patrick Department of Ophthalmology, Faculty of Medicine and Health Sciences, Universiti Malaysia Sabah, Sabah, Malaysia https://orcid.org/0000-0001-9748-2760
  • Yeap Boon Tat Department of Anesthesiology and Intensive Care, Faculty of Medicine and Health Sciences, Universiti Malaysia Sabah, Sabah, Malaysia
  • Muhamad Zarif Mohd Amin Department of Ophthalmology, Queen Elizabeth Hospital, Sabah, Malaysia
  • Maftuhim Addenan Department of Ophthalmology, Queen Elizabeth Hospital, Sabah, Malaysia
  • Shuaibah Ab.Ghani Department of Ophthalmology, Faculty of Medicine and Health Sciences, Universiti Malaysia Sabah, Sabah, Malaysia
  • Hanida Hanafi Department of Ophthalmology, Queen Elizabeth Hospital, Sabah, Malaysia; Oculoplastic and Reconstructive Unit, Department of Ophthalmology, Queen Elizabeth Hospital, Sabah, Malaysia

DOI:

https://doi.org/10.13181/mji.cr.236936

Keywords:

enophthalmos, esotropia, meningioma, ophthalmoplegia

Abstract

Primary optic nerve sheath meningioma is generally a benign tumor. In rare instances, however, the growth rate and intraocular and intracranial extensions can be highly aggressive, especially in children, leading to poor prognosis. Here, we reported a case of a 24-year-old woman who presented with left eye swelling for 3 years. This was associated with blurred vision, retrobulbar pain, and redness. On examination, the left eye was severely proptosed with complete ophthalmoplegia. Magnetic resonance imaging showed an extensive tumor occupying the whole left orbital cavity with a disfigured eyeball. However, no intracranial extension was observed. Interestingly, complete surgical excision was feasible via transconjunctival anterior orbitotomy without bone removal. The histopathological examination confirmed the diagnosis of optic nerve sheath meningioma. Adjunct radiotherapy was given. On a follow-up after 2 years, left enophthalmos with esotropia was observed.

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Published

2023-11-01

How to Cite

1.
Patrick S, Tat YB, Amin MZM, Addenan M, Ab.Ghani S, Hanafi H. Atypical orbital primary optic nerve sheath meningioma with severe disfiguring proptosis: an alternative surgical approach. Med J Indones [Internet]. 2023Nov.1 [cited 2024Dec.11];32(3):190-3. Available from: https://mji.ui.ac.id/journal/index.php/mji/article/view/6936

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Section

Case Report/Series
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